ea0030p38 | (1) | BSPED2012
Gevers Evelien
, Shah Pratik
, Meredith Suzanne
, Torpiano John
, Slater Olga
, White Anne
, Dattani Mehul
Cushings syndrome due to ectopic ACTH production is extremely rare in childhood. Ectopic ACTH secretion is most often due to tumours in the chest, but rare cases of carcinoid tumours, neuroblastoma, phaeochromocytoma and pancreatic and ovarian carcinoma have been reported. We describe a 2 year old girl with ectopic Cushings syndrome due to a malignant epithelial abdominal tumour producing POMC. She presented with rapid weight gain, hypertension, body odour, letharg...